“Castleman病”的版本间的差异
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==关系== | ==关系== | ||
| − | === | + | ===病因=== |
| − | [[Castleman病- | + | [[Castleman病-病因-细胞因子调节异常|细胞因子调节异常]]、[[Castleman病-病因-病毒感染|病毒感染]]、[[Castleman病-病因-人类8型疱疹病毒(HHV-8)感染|人类8型疱疹病毒(HHV-8)感染]]、[[Castleman病-病因-慢性抗原刺激|慢性抗原刺激]]、[[Castleman病-病因-EB病毒感染|EB病毒感染]] |
| − | === | + | ===鉴别诊断=== |
| − | [[Castleman病- | + | [[Castleman病-鉴别诊断-神经鞘瘤|神经鞘瘤]]、[[Castleman病-鉴别诊断-感染|感染]]、[[Castleman病-鉴别诊断-淋巴瘤|淋巴瘤]]、[[Castleman病-鉴别诊断-血管外皮细胞瘤|血管外皮细胞瘤]]、[[Castleman病-鉴别诊断-异位嗜铬细胞瘤|异位嗜铬细胞瘤]]、[[Castleman病-鉴别诊断-肉瘤|肉瘤]]、[[Castleman病-鉴别诊断-神经节细胞瘤|神经节细胞瘤]]、[[Castleman病-鉴别诊断-转移瘤|转移瘤]] |
| − | === | + | ===相关(导致)=== |
| − | [[Castleman病- | + | [[Castleman病-相关(导致)-POEMS综合征|POEMS综合征]]、[[Castleman病-相关(导致)-肾功能不全|肾功能不全]]、[[Castleman病-相关(导致)-副肿瘤性天疱疮|副肿瘤性天疱疮]] |
| − | === | + | ===临床表现=== |
| − | [[Castleman病- | + | [[Castleman病-临床表现-水疱|水疱]]、[[Castleman病-临床表现-发热|发热]]、[[Castleman病-临床表现-肝大|肝大]]、[[Castleman病-临床表现-淋巴结肿大|淋巴结肿大]]、[[Castleman病-临床表现-明显非均质强化|明显非均质强化]]、[[Castleman病-临床表现-肿块|肿块]]、[[Castleman病-临床表现-口眼干|口眼干]]、[[Castleman病-临床表现-肾损伤|肾损伤]]、[[Castleman病-临床表现-颈部淋巴结肿大|颈部淋巴结肿大]]、[[Castleman病-临床表现-淋巴组织增生|淋巴组织增生]]、[[Castleman病-临床表现-器官肿大|器官肿大]]、[[Castleman病-临床表现-小点状钙化灶|小点状钙化灶]]、[[Castleman病-临床表现-肾功能异常|肾功能异常]]、[[Castleman病-临床表现-脾大|脾大]]、[[Castleman病-临床表现-明显强化的肿块|明显强化的肿块]]、[[Castleman病-临床表现-双下肢水肿|双下肢水肿]]、[[Castleman病-临床表现-明显均质的强化|明显均质的强化]]、[[Castleman病-临床表现-血小板减少|血小板减少]]、[[Castleman病-临床表现-多浆膜腔积液|多浆膜腔积液]]、[[Castleman病-临床表现-口腔溃疡|口腔溃疡]]、[[Castleman病-临床表现-特征组织形态改变|特征组织形态改变]]、[[Castleman病-临床表现-口腔黏膜增生物或肿块(如Castleman病)、水疱|口腔黏膜增生物或肿块(如Castleman病)、水疱]]、[[Castleman病-临床表现-不明原因淋巴结肿大|不明原因淋巴结肿大]] |
===发病部位=== | ===发病部位=== | ||
| − | [[Castleman病-发病部位-颈部|颈部]] | + | [[Castleman病-发病部位-纵膈|纵膈]]、[[Castleman病-发病部位-腹部|腹部]]、[[Castleman病-发病部位-颈部|颈部]] |
| + | |||
| + | ===相关(症状)=== | ||
| + | [[Castleman病-相关(症状)-假性瘤|假性瘤]] | ||
| + | |||
| + | ===药物治疗=== | ||
| + | [[Castleman病-药物治疗-糖皮质激素|糖皮质激素]]、[[Castleman病-药物治疗-沙利度胺|沙利度胺]]、[[Castleman病-药物治疗-甲泼尼龙|甲泼尼龙]]、[[Castleman病-药物治疗-长春地辛|长春地辛]] | ||
===化疗=== | ===化疗=== | ||
| − | [[Castleman病-化疗-生物治疗|生物治疗]]、[[Castleman病- | + | [[Castleman病-化疗-术后辅助化疗|术后辅助化疗]]、[[Castleman病-化疗-化疗|化疗]]、[[Castleman病-化疗-生物治疗|生物治疗]] |
| + | |||
| + | ===预后状况=== | ||
| + | [[Castleman病-预后状况-较差|较差]]、[[Castleman病-预后状况-较好|较好]] | ||
| + | |||
| + | ===组织学检查=== | ||
| + | [[Castleman病-组织学检查-颈部淋巴结活检|颈部淋巴结活检]]、[[Castleman病-组织学检查-病理活检|病理活检]]、[[Castleman病-组织学检查-骨髓穿刺活检|骨髓穿刺活检]]、[[Castleman病-组织学检查-活检|活检]]、[[Castleman病-组织学检查-淋巴结活检|淋巴结活检]] | ||
| − | === | + | ===同义词=== |
| − | [[Castleman病- | + | [[Castleman病-同义词-Castleman's disease|Castleman's disease]]、[[Castleman病-同义词-Castleman disease|Castleman disease]]、[[Castleman病-同义词-CD|CD]]、[[Castleman病-同义词-血管滤泡性淋巴结增生|血管滤泡性淋巴结增生]]、[[Castleman病-同义词-巨大淋巴结增生症|巨大淋巴结增生症]]、[[Castleman病-同义词-血管滤泡型|血管滤泡型]] |
| − | === | + | ===辅助检查=== |
| − | [[Castleman病- | + | [[Castleman病-辅助检查-肌电图|肌电图]]、[[Castleman病-辅助检查-眼科检查|眼科检查]]、[[Castleman病-辅助检查-心脏彩超|心脏彩超]] |
===病理分型=== | ===病理分型=== | ||
| − | [[Castleman病-病理分型- | + | [[Castleman病-病理分型-多中心型|多中心型]]、[[Castleman病-病理分型-浆细胞型Castleman病|浆细胞型Castleman病]]、[[Castleman病-病理分型-淋巴组织增生性疾病|淋巴组织增生性疾病]]、[[Castleman病-病理分型-Ⅲ型(混合型)|Ⅲ型(混合型)]]、[[Castleman病-病理分型-Ⅱ型(浆细胞型)|Ⅱ型(浆细胞型)]]、[[Castleman病-病理分型-单中心型|单中心型]]、[[Castleman病-病理分型-单中心型Castleman病|单中心型Castleman病]]、[[Castleman病-病理分型-多中心型混合型Castleman病|多中心型混合型Castleman病]]、[[Castleman病-病理分型-局灶型浆细胞型Castleman病|局灶型浆细胞型Castleman病]]、[[Castleman病-病理分型-局灶型Castleman病|局灶型Castleman病]]、[[Castleman病-病理分型-局限型|局限型]]、[[Castleman病-病理分型-浆细胞型|浆细胞型]]、[[Castleman病-病理分型-透明血管型|透明血管型]]、[[Castleman病-病理分型-混合型|混合型]]、[[Castleman病-病理分型-局灶型|局灶型]]、[[Castleman病-病理分型-泛发型|泛发型]] |
| + | |||
| + | ===手术治疗=== | ||
| + | [[Castleman病-手术治疗-手术切除|手术切除]]、[[Castleman病-手术治疗-手术治疗|手术治疗]]、[[Castleman病-手术治疗-切除肿瘤|切除肿瘤]]、[[Castleman病-手术治疗-肺移植|肺移植]]、[[Castleman病-手术治疗-肿瘤切除|肿瘤切除]] | ||
===放射治疗=== | ===放射治疗=== | ||
[[Castleman病-放射治疗-放疗|放疗]] | [[Castleman病-放射治疗-放疗|放疗]] | ||
| − | === | + | ===影像学检查=== |
| − | [[Castleman病- | + | [[Castleman病-影像学检查-X线|X线]]、[[Castleman病-影像学检查-18F-FDG PET/CT|18F-FDG PET/CT]]、[[Castleman病-影像学检查-术前CT检查|术前CT检查]]、[[Castleman病-影像学检查-CT|CT]]、[[Castleman病-影像学检查-MR|MR]]、[[Castleman病-影像学检查-CT影像|CT影像]]、[[Castleman病-影像学检查-PET-CT|PET-CT]]、[[Castleman病-影像学检查-CT检查|CT检查]]、[[Castleman病-影像学检查-超声|超声]] |
| − | |||
| − | |||
| − | [[Castleman病- | ||
| − | |||
| − | |||
| − | [[Castleman病- | ||
===发病年龄=== | ===发病年龄=== | ||
| − | [[Castleman病-发病年龄-7~74岁|7~74岁]] | + | [[Castleman病-发病年龄-7~74岁|7~74岁]]、[[Castleman病-发病年龄-55岁男性|55岁男性]] |
| − | === | + | ===实验室检查=== |
| − | [[Castleman病- | + | [[Castleman病-实验室检查-免疫组织化学|免疫组织化学]]、[[Castleman病-实验室检查-淋巴结病理学检查|淋巴结病理学检查]]、[[Castleman病-实验室检查-组织化学|组织化学]]、[[Castleman病-实验室检查-血清免疫固相电泳|血清免疫固相电泳]]、[[Castleman病-实验室检查-HHV-8 DNA定量检测|HHV-8 DNA定量检测]]、[[Castleman病-实验室检查-免疫组织化学检测|免疫组织化学检测]] |
| − | === | + | ===并发症=== |
| − | [[Castleman病- | + | [[Castleman病-并发症-副肿瘤天疱疮|副肿瘤天疱疮]]、[[Castleman病-并发症-天疱疮|天疱疮]]、[[Castleman病-并发症-闭塞性细支气管炎|闭塞性细支气管炎]] |
2022年9月22日 (四) 13:56的版本
目录
实体介绍
待补充
关系
病因
细胞因子调节异常、病毒感染、人类8型疱疹病毒(HHV-8)感染、慢性抗原刺激、EB病毒感染
鉴别诊断
神经鞘瘤、感染、淋巴瘤、血管外皮细胞瘤、异位嗜铬细胞瘤、肉瘤、神经节细胞瘤、转移瘤
相关(导致)
临床表现
水疱、发热、肝大、淋巴结肿大、明显非均质强化、肿块、口眼干、肾损伤、颈部淋巴结肿大、淋巴组织增生、器官肿大、小点状钙化灶、肾功能异常、脾大、明显强化的肿块、双下肢水肿、明显均质的强化、血小板减少、多浆膜腔积液、口腔溃疡、特征组织形态改变、口腔黏膜增生物或肿块(如Castleman病)、水疱、不明原因淋巴结肿大
发病部位
相关(症状)
药物治疗
化疗
预后状况
组织学检查
同义词
Castleman's disease、Castleman disease、CD、血管滤泡性淋巴结增生、巨大淋巴结增生症、血管滤泡型
辅助检查
病理分型
多中心型、浆细胞型Castleman病、淋巴组织增生性疾病、Ⅲ型(混合型)、Ⅱ型(浆细胞型)、单中心型、单中心型Castleman病、多中心型混合型Castleman病、局灶型浆细胞型Castleman病、局灶型Castleman病、局限型、浆细胞型、透明血管型、混合型、局灶型、泛发型
手术治疗
放射治疗
影像学检查
X线、18F-FDG PET/CT、术前CT检查、CT、MR、CT影像、PET-CT、CT检查、超声
发病年龄
实验室检查
免疫组织化学、淋巴结病理学检查、组织化学、血清免疫固相电泳、HHV-8 DNA定量检测、免疫组织化学检测